Hint | Answer |
tightness of skin, loss of wrinkles on fingers | |
What percent of people with early complement deficiency develop lupus | |
Which HLA subtype is associated with ankylosing spondylitis | |
APA plus hypercoaguble state is called | |
immunodysregulation polyendocrinopathy enteropathy X-linked | |
Most common Ig deficiency | |
Contract would during granulation | |
Which antibody produces a false positive test for syphillis | |
Autoimmune lymphoproliferative syndrome is cause by a defect in what pathway | |
What is the marker for hematopoietic stem cells | |
Fibroblast growth factor, inhibits inflammation | |
Infections in CVID and X linked agammaglobulinemia pts | |
Provide nutrients during granulation | |
What type of collagen makes up cartilage | |
Antibodies are to what in diffuse scleroderma | |
Cell surface marker for monocyte lineage (macrophages) | |
Mutatated protein in X linked agammaglobulinemia | |
Tissue that is quiescent but can reenter cell cycle | |
What is the stem cell of the lung | |
Disease with low IgG due to defects in B or T cells | |
Antigen-antibody complex (Type III) deposition on multiple tissue | |
Most common cause of death in diffuse scleroderma involves what organ | |
What is necessary for hydroxylation of glycine and lysine | |
Thrombocytopenia, eczema, reccurent infections | |
Epithelial and fibroblast growth factor | |
Of dry eyes/mouth, ANA/ASSA/ASSB, and biopsy, how many need to be positive for Dx of Sjogrens | |
Tx of DiGeorge pt | |
Where are the stem cells for the skin | |
What type of hypersensitivity is Sjogren's | |
Most common and most sever renal injury for SLE pts | |
Autoantibodies present in Sjogrens syndrome, Anti- | |
What is the 5 year survival for SLE | |
CREST symptoms are for what subtype of scleroderma | |
Antibodies against host nuclear material | |
Do drug induced SLE pts get renal damage commonly? | |
Anemia, thromboytopenia, and leukopenia are due to what type of hypersensitivity in SLE | |
What cytokine is necessary for survival of Tregs | |
What is a hypertrophic scar made up of predominantly | |
What type of collagen makes up vasculature, granulation tissue, embryonic tissue | |
What part of the thymus does positive selection occur | |
Tyrosine phosphatase that has mutations associated with autoimmune disorders | |
Drug that induces SLE (Smooth muscle relaxant) | |
Which Anti-ANA has prognostic value and predics renal damage | |
Second most common cause of death in diffuse scleroderma involves what organ | |
What is present in the serum of pts with Sjogrens | |
What deficiency disposes an individual to SLE | |
How long after birth do XLG babies present with symptoms | |
What disease is highly associated with IgA deficiency | |
Lymphocytic destruction of salivary and lacrimal glands | |
ANA with serum antibodies against U1 ribonucleoprotein | |
Oral or nasopharyngeal ulcers, discoid rash, arthritis, peripheral vasospasm | |
What must be avoided in XLG babies | |
Are drug induced SLE pts ANA+ | |
What is increased in Scleroderma that is a potent vasocontrictor | |
What type of cells suppress Tcells by competitive binding of CTLA4 to CD28 | |
Child with two very swollen eylids | |
What type of selection is the checkpoint between double positive and single positive cells, also called MHC restriction | |
Sudden onset of acute renal failure and hypertension, diffuse scleroderma | |
Most commonly involved organ system in diffuse scleroderma | |
Which ANA are specific for lupus | |
African american females, CNS psychosis, renal damage | |
Drug that induces SLE (Antiarrythmic) | |
Is APA syndrome more commonly primary or secondary to SLE? | |
Cells that present single positive cells with many self antigens | |
Receptor editing in B cells is facilitated by which gene | |
What element is necessar for collagenase to remove type III collagen | |
Lack of thymus, lack of parathyroids, abnormalities in heart, great vessels, face | |
Etiology in SCID (enzyme) | |
R in CREST | |
Developmental failure of 3d and 4th pouches | |
CD4+ CD25+(IL2r) FoxP3+ | |
What is the cardiovascular complication for late SLE | |
What is necessary for crosslinking of glycine and lysine by lysyl oxidase | |
Etiology in SCID (cell surface) | |
Endothelium, smooth muscle, fibroblast growth factor | |
E in CREST | |
In scar formation, type III collagen is replaced by what type of collagen | |
Antibodies are to what in limited scleroderma | |
What are Sjogrens pts at a higher risk for late in the disease | |
What type of collagen is in the basement membrane | |
Disease with mutated CD40L or CD40, no class switching | |
Deficiency in C5-C9, increased risk for infections with ? | |
What part of the thymus does negative selection occur | |
Growth factor in angiogenesis | |
Selection type in thymus that checks binding to self antigen | |
Features of SLE, Systemic sclerosis, polymyositis, autoimmune | |
What are the specific Anti-ribonucleoproteins, Anti- | |
C in CREST | |
Polyendocrine syndrome is caused by a mutation in what protein | |
Initial phase of repair | |
Hardening of tissue, deposition of collagen, systemic | |
Small vegetation on both sides of mitral valve | |
T in CREST | |
Binding of antigen by CD4 cell without second signal leads to what | |
Defective cell mediated and humoral immunities | |
Growth factor in angiogenesis, skeletal development | |
Deposit type III collagen during granulation | |
Where are the stem cells for the bowels | |
Inheritance pattern for Wiskott-aldrich syndrome | |
What does the biopsy exclude as causes for destruction of salivary gland | |
What would be seen on biopsy that is diagnostic of Sjogrens | |
IPEX syndrome is caused by mutations in what? | |
Complete lack of Ig's | |
S in CREST | |
What does a keloid have excess of | |
Hereditary angioedema of skin, periorbital membranes, and mucosal surfaces | |
Libman-Sacks endocarditis, Arthritis | |
Drug that induces SLE (TB Tx) | |
What can anti SSA,SSB cause in children | |
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